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Multifocal Paraganglioma in Teenager Presenting with Hypertension

Published:October 21, 2022DOI:https://doi.org/10.1016/j.urology.2022.10.006

      Abstract

      Pediatric hypertension represents a rare though increasingly common medical problem. When encountered, a workup to determine the etiology should be conducted. In this report, we detail an unusual case in which a teenager presenting with hypertension was found to have multifocal paragangliomas. We illustrate important considerations in management which include appropriate preoperative labs and imaging, collaboration with endocrinology for preoperative alpha-blockade, surgical management with close perioperative hemodynamic control, and genetic evaluation for patients with multifocal disease, diagnosis at early age, or family history as these cases are often associated with genetic alterations and other syndromes.

      KEYWORDS

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