Abstract
Pediatric hypertension represents a rare though increasingly common medical problem.
When encountered, a workup to determine the etiology should be conducted. In this
report, we detail an unusual case in which a teenager presenting with hypertension
was found to have multifocal primary paragangliomas. We illustrate important considerations
in management which include appropriate preoperative labs and imaging, collaboration
with endocrinology for preoperative alpha-blockade, surgical management with close
perioperative hemodynamic control, and genetic evaluation for all patients with paragangliomas.
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References
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Further Reading
- Genetics and clinical characteristics of hereditary pheochromocytomas and paragangliomas.Endocr Relat Cancer. 2011; 18: R253-R276
Article info
Publication history
Published online: October 21, 2022
Accepted:
October 9,
2022
Received:
October 3,
2022
Publication stage
In Press Journal Pre-ProofFootnotes
Financial Disclosures: None.
Identification
Copyright
© 2022 Published by Elsevier Inc.
