Abstract
Prune belly syndrome (PBS) is a rare but morbid complexity of congenital anomalies
that consists of abdominal wall defect, bilateral cryptorchidism, and urinary tract
dilation. With the recent advances in perinatal care, the life expectancy of patients
with PBS has improved. Although renal and sexual outcomes are frequently discussed
in the literature, little is known about urinary tract malignancies in adulthood.
Herein, we present a case of advanced bladder cancer in a 38-year-old man with PBS.
To the best of our knowledge, a malignant tumor arising in a nondefunctionalized or
nonaugmented bladder in patients with PBS has not been reported previously.
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Article info
Publication history
Published online: December 06, 2021
Accepted:
November 29,
2021
Received:
September 1,
2021
Footnotes
Financial Disclosure: The authors declare that they have no relevant financial interests.
Identification
Copyright
© 2021 Elsevier Inc. All rights reserved.
