Ovotesticular Disorder Mimicking Acute Spermatic Cord Torsion

Published:November 28, 2021DOI:


      Ovotesticular disorder is a rare form of sexual development in which a patient may have one ovary and one testis, or more commonly a gonad or gonads containing both ovarian and testicular tissue. Patients with this condition typically present in infancy with ambiguous genitalia. Delayed presentations of clinically symptomatic, older patients with normal external genitalia are extremely rare. We present a case of a 14-year-old male with normal external genitalia who presented with symptoms and signs consistent with spermatic cord torsion but found to have ovotesticular disorder on evaluation.
      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'


      Subscribe to Urology
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect


        • Walker AM
        • Walker J
        • Adams S
        • et al.
        True hermaphroditism.
        J Paediatr Child Health. 2000; 36: 69-73
        • Wettasinghe KT
        • Sirisena ND
        • Andraweera PH
        • et al.
        A case series of five Sri Lankan patients with ovotesticular disorder of sex development.
        Clin Pediatr Endocrinol. 2012; 21: 69-73
        • Diamond DA
        Sexual differentiation: normal and abnormal.
        in: Wein AJ Kavoussi LR Novick AC Partin AW Peters CA Campbell-Walsh Urology. 9th ed. Saunders Elsevier, Philadelphia, PA2007: 3799-3829
        • Mittwoch U.
        Genetics of sex determination: exceptions that prove the rule.
        Mol Genet Metab. 2000; 71: 405
        • Ceci M
        • Calleja E
        • Said E
        • Gatt N.
        A case of true hermaphroditism presenting as a testicular tumour.
        Case Rep Urol. 2015; 2015598138
        • Kropp BP
        • Keating MA
        • Moshang T
        • et al.
        True hermaphroditism and normal male genitalia: an unsual presentation.
        Urology. 1995; 46: 736-739
        • Eberenz W
        • Kotlus Rosenberg H
        • Moshang T
        • et al.
        True hermaphroditism: sonographic demonstration of ovotestes.
        Radiology. 1991; 179: 429-431
        • Ali Mirshahvalad S
        • Alinia P
        • Hekmati A
        • et al.
        Ovotesticular disorder of sex development presenting as an acute scrotum.
        Urology. 2018; 116: 176-179
        • Scarpa MG
        • Grazia MD
        • Tornese G.
        46,XY ovotesticular disorders of sex development: a therapeutic challenge.
        Pediatr Rep. 2017; 9: 7085
        • Finlayson C
        • Fritsch MK
        • Johnson EK
        • et al.
        Presence of germ cells in disorders of sex development: implications for fertility potential and preservation.
        J Urol. 2017; 197: 937-943