Pediatric Case Reports| Volume 159, P210-213, January 2022

Congenital Giant Megaureter in a 16-Year-Old Female Presenting With Abdominal Pain: A Case Report and Review of Literature

Published:October 30, 2021DOI:


      We describe a case of congenital giant megaureter in a 16-year-old female. She presented with a 5-day history of abdominal distention, right flank pain and tenderness. Right pyelonephritis was suspected. Computerized tomography showed a large cystic abdominal mass with no appreciably functioning left kidney causing secondary compression of the contralateral right ureter. A left upper nephroureterectomy was performed, draining over 3.5 L of fluid. Our experience suggests that congenital giant megaureter should be considered in the differential for pediatric patients presenting with a cystic abdominal mass.
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        • Annigeri VM
        • Hegde HV
        • Patil PB
        • et al.
        Congenital giant megaureter with duplex kidney presenting as abdominal lump in a neonate.
        J Indian Assoc Pediatr Surg. 2012; 17: 168-170
        • Huang CJ
        Congenital giant megaureter.
        J Pediatr Surg. 1987; 22: 235-239
        • Yu M
        • Ma G
        • Ge Z
        • et al.
        Unilateral congenital giant megaureter with renal dysplasia compressing contralateral ureter and causing bilateral hydronephrosis: a case report and literature review.
        BMC Urol. 2016; 16: 7
        • Stoll C
        • Alembik Y
        • Roth MP
        • et al.
        Risk factors in internal urinary system malformations.
        Pediatr Nephrol. 1990; 4: 319-323
        • Anheuser P
        • Kranz J
        • Steffens J
        • et al.
        Primärer Megaureter.
        Urologe. 2013; 52: 33-38
        • Merlini E
        • Spina P
        Primary non-refluxing megaureters.
        J Pediatr Urol. 2005; 1: 409-417
        • Farrugia M-K
        • Hitchcock R
        • Radford A
        • et al.
        British Association of Paediatric Urologists consensus statement on the management of the primary obstructive megaureter.
        J Pediatr Urol. 2014; 10: 26-33
        • Smith ED
        • Cussen IJ
        • Glenn J
        Report of working party to establish an international nomenclature for the large ureter.
        Birth Defects Orig Artic Ser. 1977; 13: 3-8
        • Shokeir AA
        • Nijman RJ m
        Primary megaureter: current trends in diagnosis and treatment.
        BJU International. 2000; 86: 861-868
        • Tsukahara H
        • Ando T
        • Fujii Y
        • et al.
        Giant hydroureteronephrosis associated with primary obstructed megaureter.
        Acta Paediatr Jpn. 1991; 33: 723-728
        • Ramaswamy S
        • Bhatnagar V
        • Mitra DK
        • et al.
        Congenital segmental giant megaureter.
        J Pediatr Surg. 1995; 30: 123-124
        • Lelli-Chiesa P
        • Cupaioli M
        • Rossi C
        • et al.
        Congenital giant megaureter: first neonatal case.
        J Pediatr Surg. 2001; 36: 944-945
        • Goto H
        • Kanematsu A
        • Yoshimura K
        • et al.
        Preoperative diagnosis of congenital segmental giant megaureter presenting as a fetal abdominal mass.
        J Pediatr Surg. 2010; 45: 269-271
        • Saurabh G
        • Lahoti BK
        • Geetika P
        Giant megaureter presenting as cystic abdominal mass.
        Saudi Journal of Kidney Diseases and Transplantation. 2010; 21: 160
        • Khattar N
        • Dorairajan LN
        • Kumar S
        • et al.
        Giant obstructive megaureter causing contralateral ureteral obstruction and hydronephrosis: a first-time report.
        Urology. 2009; 74: 1306-1308